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Literature summary for 1.2.1.47 extracted from

  • Almannai, M.; Alfadhel, M.; El-Hattab, A.W.
    Carnitine inborn errors of metabolism (2019), Molecules, 24, 3251 .
    View publication on PubMedView publication on EuropePMC

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
4-trimethylammoniobutanal + NAD+ + H2O Homo sapiens
-
4-trimethylammoniobutanoate + NADH + 2 H+
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
4-trimethylammoniobutanal + NAD+ + H2O
-
Homo sapiens 4-trimethylammoniobutanoate + NADH + 2 H+
-
?

Synonyms

Synonyms Comment Organism
4-N-trimethylaminobutyraldehyde dehydrogenase
-
Homo sapiens
TMABA dehydrogenase
-
Homo sapiens
TMABADH
-
Homo sapiens

Cofactor

Cofactor Comment Organism Structure
NAD+
-
Homo sapiens